Hemifacial hypertrophy abbreviated as (HFH) is rare congenital disease characterized by unilateral enlargement of the head and teeth. It is classified as true. Depending on involvement of soft tissues, teeth, and bones, he further classified hemifacial hypertrophy into (a) true hemifacial hypertrophy and. Two cases of congenital hemifacial hypertrophy are described. To our knowledge , this is the first report of this syndrome in a black African population. Possible.

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Hemifacial hypertrophy

An extensive search of the English language literature revealed no formal reports of malignant transformation. It was clear that there was a unilateral enhancement of development on this side. The enlargement extended from the midline to the preauricular region, superiorly to the frontal bone and inferiorly to the inferior border of mandible. Ipsilateral pinna and pupil may be enlarged, but an increase in size of the inner ear or globe of the eye has not been reported [ 4 ].

Clinical and Imaging Findings of True Hemifacial Hyperplasia

The patient, however, was adamant and wished hypeftrophy treatment only if complete symmetry could be achieved. Review and report of two cases. This movement mimics action during traditional suction-assisted liposuction due to which, surgeons experience less fatigue during power liposuction with easier penetration and removal of adipose tissue. Burchfield and Escobar described a family in which several members showed mandibular asymmetry and maxillary hypoplasia.


Congenital hemifacial hyperplasia

Enlargement and deformity of all tissue of the face, including teeth and their related tissues in the jaw, are the key findings in the diagnosis of hemifacial hypertrophy 5. These asymmetries are often noted at birth and are usually accentuated with increasing age, especially around puberty 2. Intraoral examination disclosed an obvious alveolar enlargement of the right maxillary and mandibular quadrants as compared to the left quadrants Figure 2.

Abstract Congenital hemihyperplasia is a rare developmental disorder characterized by unilateral overgrowth of one or more body parts resulting in marked asymmetry. Widening of hemifaciao palate and enlargement of the alveolar bone of the affected hemiracial were noted in the present case as described in the literature [ 4 ].

Competing Interests The authors declare that they have no competing interests. A thirty-nine-year-old male patient reported to the Department of Oral Medicine and Radiology with a chief complaint of asymptomatic swelling in his right cheek region since birth.

Journal List Case Rep Dent v. Hemifacial hypertrophy This condition is inherited in an autosomal dominant manner [1] Hemifacial hypertrophy also termed facial hemihypertrophy[2] facial hemihyperplasia[2] or Friedreich’s disease [3] abbreviated as HFH is rare congenital disease characterized by unilateral enlargement of the head and teeth.

Periodontium gingivaperiodontal ligamentcementumalveolus — Gums and tooth-supporting structures.

You can also scroll through stacks with your mouse wheel or the keyboard arrow keys. Patient showed mild tenderness on the right condylar region. Hemifacail diagnosis of facial hemihyperplasia includes fibrous dysplasia, dyschondroplasia, congenital lymph edema, arteriovenous aneurysm, hemangioma, lymphangioma, neurofibromatosis, and malignant lesions osteosarcoma and chondrosarcoma.


Unfortunately, it is not free to produce. Treatment is not indicated hypeftrophy HFH unless cosmetic considerations are involved. Am J Med Sci. Later, a small amount of fluid was introduced into the fat wet liposuction. Hemifacial myohyperplasia is also newly proposed and described as a separate entity in which there is predominantly hyperplasia of the facial musculature.

Hemifacial hypertrophy | Radiology Reference Article |

Tommasi AF, Jitomirski F. Basal cell adenoma Canalicular adenoma Ductal papilloma Monomorphic adenoma Myoepithelioma Oncocytoma Papillary cystadenoma lymphomatosum Pleomorphic adenoma Sebaceous adenoma Malignant: A diverse form of hemifacial hyperplasia. We are reporting here, a case of true hemifacial hypertrophy in a young female adult highlighting the clinical features and possible treatment options. Declaration of patient consent The authors certify that they have obtained all appropriate patient consent forms.

Report of two cases. Our patient demonstrated both hyperplasia of the muscles of mastication and presence of lipomas along with involvement of bones and teeth.

Axial CT scan with bone reconstructions showing widened foramen ovale right side-arrow, left side-arrowhead. Occurrence of small exostoses of the posterior auditory canal has also been reported [ 12 ].