Esferocitosis hereditaria. Carolina Cózar Trastorno hemolítico familiar caracterizado por: anemia ictericia intermitente esplenomegalia. Esferocitosis Hereditaria Anemia Esferocitosis Hereditaria 1) Defecto de la membrana del eritrocito. 2) Retención selectiva por el bazo normal. De esta forma es posible el rastreo de la esferocitosis hereditaria y de la Las manifestaciones clínicas como ictericia, esplenomegalia, anemia, aplasia y y sobrecarga de hierro sugiere daño pancréatico por la acumulación, tal como se.

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Hereditary spherocytosis, thrombocytosis, and chronic pulmonary emboli: Splenectomy for hereditary spherocytosis: Clinical symptoms such as jaundice, splenomegaly, anemia, aplasia and biliary calculi prompting a diagnosis of HS are in reality rare.

Thrombo-embolic disease after splenectomy for hereditary stomatocytosis. Se recomienda el monitoreo de glucemia y ferritina.

Erythroid membrane protein defects in hereditary spherocytosis. A study of 62 Spanish cases.

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J Thromb Thrombolysis ;17 3: Patient esferocitodis physician should be informed of the presence of HS to avoid misinterpretation of concurrent pathological symptoms.

Laparoscopic partial vs total splenectomy in children with hereditary spherocytosis. The Italian survey on hereditary spherocytosis. Long-term evaluation of the beneficial effect of subtotal splenectomy for management of hereditary spherocytosis.


This explains the discrepancy between these values. Este hecho explica la discrepancia entre estos valores.

Am J Hematol ;57 1: Oxygen affinity and compensated hemolysis in hereditary spherocytosis. Int J Pediatr Hematol Oncol ; 2: Guidelines for the diagnosis and management of hereditary spherocytosis update. esferovitosis

Anemia Esferocitosis Hereditaria by Danna flores cuadros on Prezi

Revista Cubana Hematol Inmunol Hemoter ;18 1: Hereditary Spherocytosis in Neonates with Hyperbilirubinemia. Applying criteria such as permanence of an increased percentage of spherocytes, family history, biochemical symptoms of hemolysis and clinical data, we claim a prevalence of generally asymptomatic hereditary spherocytosis HS of 1: Servicio de ayuda de la revista. Thus it esferocitosie possible to screen for both hereditary and secondary spherocytosis. Bienvenido a siicsalud Contacto Inquietudes.

Br J Haematol ;93 2: HS being a hemolytic defect, frequently increased iron overload was not unexpected. Abstract Hematological automates using double beam laser diffraction by artificially spherized red blood cells determine both volume and hemoglobin concentration of a very large number of cells, even indicating percentages of aberrant elements.

Postoperative pulmonary embolism in a young female accompanying with Factor V Leiden mutation and hereditary sypherocytosis. The high association of HS with both diabetes and iron overload suggest damage of the endocrine pancreas by the latter, as it is also seen in genetic esferociitosis.


Aires, Argentina; 16 2: Monitoring of blood glucose and ferritin is recommended. Polish Academjy of Sciences?

Esferocitosis hereditaria by Jazmin Cózar Madero on Prezi

Clinico-hematological profile of hereditary spherocytosis: De esta forma es posible el rastreo de la esferocitosis hereditaria y de la esferocitosis secundaria. The identity of hyperchromic RBC and spherocytes as well as their normal percentage have been previously established. Blood Cells Mol Dis ; King on behalf of the General Haematology Task Force of the British Committee for Standards in Haematology Guidelines for the diagnosis and management of hereditary spherocytosis.

J Lab Clin Med. Journal of Medical Cases. Referencias -Mayelin Herrera Garcia.